Management of Red Teeth in an International Patient with X-Linked Adrenoleukodystrophy

Petrova, Elena; Miller, Weston P.; Myers, Sandra L.; Karp, Jeffrey M.
November 2015
Pediatric Dentistry;Nov/Dec2015, Vol. 37 Issue 7, p550
Academic Journal
journal article
Childhood cerebral X-linked adrenoleukodystrophy is a progressive, central nervous system, and endocrine disorder that typically leads to total neurologic disability and, eventually, death without appropriate, timely medical therapy. Hematopoietic stem cell transplantation has been found effective in slowing cerebral deterioration and improving long-term survival. The purpose of this case report was to describe the multidisciplinary management of red, discolored, pulpally treated primary molars identified in a nine-year-old Russian boy with childhood cerebral X-linked adrenoleukodystrophy preparing for myeloablative conditioning chemotherapy followed by hematopoietic stem cell transplantation.


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