Diffuse Hemangiomatosis of the Spleen: Splenic Hemangiomatosis Presenting with Giant Splenomegaly, Anemia, and Thrombocytopenia

Shiran, A.; Naschitz, J. E.; Yeshurun, D.; Misselevitch, I.; Boss, J. H.
November 1990
American Journal of Gastroenterology;Nov1990, Vol. 85 Issue 11, p1515
Academic Journal
In an elderly patient with oligosymptomatic giant splenomegaly, clinical and laboratory data were nondiagnostic, while nonhomogeneous splenic enlargement was the only finding detected by imaging procedures. Splenectomy was performed and diffuse hemangiomatosis of predominantly capillary-type found. The failure of imaging techniques to even hint at the nature of the underlying disorder is comprehensible in view of the organ being essentially replaced in toto by the abnormal vascular channels. Diffuse splenic hemangiomatosis, a rare condition, may cause hypersplenism, and its diagnosis may be elusive because of misleading patterns on imaging.


Related Articles

  • Rubinstein Taybi Syndrome with Hepatic Hemangioma. Sahiner, U. M.; Senel, S.; Erkek, N.; Karacan, C.; Yoney, A. // Medical Principles & Practice;Mar2009, Vol. 18 Issue 2, p162 

    Objective: It was the aim of our study to present a case of Rubinstein Taybi syndome (RTS) associated with hepatic hemangioma. Clinical Presentation and Intervention: A 6.5-year-old boy was diagnosed with RTS. He had large areas of cutaneous capillary hemangiomas. Radiological examination...

  • Surgical repair in neonatal life of cardiac haemangiomas diagnosed prenatally. Sharma, Jayendra; Hirata, Yasutaka; Mosca, Ralph S. // Cardiology in the Young;Aug2009, Vol. 19 Issue 4, p403 

    Although cardiac tumours are rare, such tumours are increasingly being diagnosed with increasing frequency and great accuracy by antenatal ultrasound. Cardiac haemangiomas account for less than one- twentieth of all primary cardiac tumours, with most being diagnosed in the neonatal period. We...

  • Spinal dysraphism associated with the cutaneous lumbosacral infantile hemangioma: a neuroradiological review. Schumacher, Wendy; Drolet, Beth; Maheshwari, Mohit; Horii, Kimberly; Nopper, Amy; Newell, Brandon; Metry, Denise; Garzon, Maria; Morel, Kimberly; Chamlin, Sarah; Mancini, Anthony; Frieden, Ilona; Johnson, Craig // Pediatric Radiology;Mar2012, Vol. 42 Issue 3, p315 

    Background: Spinal dysraphism is suspected in patients with midline abnormalities, especially in those with lumbosacral cutaneous markings. A recent prospective study demonstrated that isolated cutaneous infantile hemangiomas (IH) of the lumbosacral region have one of the highest risks (relative...

  • Spontaneous subacute intratumoral hemorrhage of hepatic cavernous hemangioma. Shimoji, K.; Shiraishi, A.; Kuwatsuru, R.; Maehara, T.; Matsumoto, T.; Kurosaki, Y. // Abdominal Imaging;Jul/Aug2004, Vol. 29 Issue 4, p443 

    We report a case of giant hepatic cavernous hemangioma associated with spontaneous subacute intratumoral hemorrhage. Magnetic resonance imaging showed an oval, homogeneous, high-intensity lesion with a low-intensity rim in the original high-intensity tumor on T2-weighted images. On T1-weighted...

  • Transcatheter arterial chemoembolization in patients with hepatocellular carcinoma and coexisting hepatic cavernous hemangioma. Ran-Chou Chen; Jiunn-Ming Lii; Wei-Tsung Chen; Hsing-Yang Tu; Liang-Chung Chiang // European Radiology;Jun2006, Vol. 16 Issue 6, p1346 

    We investigated the consequence of repeated transcatheter arterial chemoembolization (TACE) for coexisting small hepatic hemangioma in the treatment of patients with hepatocellular carcinomas and describe the imaging features of embolized hemangioma on the follow-up Lipiodol CT and MR. Six of...

  • MRI and intraoperative findings in cavernous haemangiomas of the spinal cord. Weinzierl, M. R.; Krings, T.; Korinth, M. C.; Reinges, M. H. T.; Gilsbach, J. M. // Neuroradiology;Jan2004, Vol. 46 Issue 1, p65 

    More sensitive imaging techniques, such as MRI, have led to an increase in the number of reported cases of spinal cord cavernous haemangioma (SCCH). Complete surgical resection has been performed with good outcomes. However, operative findings do not always confirm preoperative MRI as to the...

  • Evaluation of shearwave elastography for the characterisation of focal liver lesions on ultrasound. Guibal, Aymeric; Boularan, Camille; Bruce, Matthew; Vallin, Mélanie; Pilleul, Frank; Walter, Thomas; Scoazec, Jean; Boublay, Nawele; Dumortier, Jérôme; Lefort, Thibaut // European Radiology;Apr2013, Vol. 23 Issue 4, p1138 

    Objectives: To determine the elasticity characteristics of focal liver lesions (FLLs) by shearwave elastography (SWE). Methods: We used SWE in 108 patients with 161 FLLs and in the adjacent liver for quantitative and qualitative FLLs stiffness assessment. The Mann-Whitney test was used to assess...

  • Symptomatic splenic hamartoma with renal, cutaneous, and hematological abnormalities. Kassarjian, A.; Patenaude, Y. G.; Bernard, C.; Bell, L. // Pediatric Radiology;Jan2001, Vol. 31 Issue 2, p111 

    Background. There is a rare association between splenic hamartomas and hematological abnormalities with, to our knowledge, only 24 reported cases in the English literature.¶Patients and methods. We report a case of a splenic hamartoma in a 14-year-old boy associated with membranoproliferative...

  • Ovarian cavernous haemangioma presenting as a heavily calcified adnexal mass. Kim, M. Y.; Rha, S. E.; Oh, S. N.; Lee, Y. J.; Jung, E. S.; Byun, J. Y. // British Journal of Radiology;Nov2008, Vol. 81 Issue 971, pe269 

    Haemangioma is an extremely rare tumour of the ovary. We describe the CT and MRI findings of a heavily calcified ovarian haemangioma in a 69-year-old woman presenting with adnexal torsion. CT showed a well-circumscribed mass with extensive punctate calcifications, located posterior to the...


Read the Article


Sorry, but this item is not currently available from your library.

Try another library?
Sign out of this library

Other Topics